Announcements Trials
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Phase

Phase 2 3Phase 4 1

Status

Recruiting 2Active not recruiting 2Available 1

Sponsor Class

INDUSTRY 3OTHER 1NETWORK 1

Study Type

Interventional 4Expanded_access 1

Sponsor

Cancer Type

Plasma cell 9Sarcoma 5Tumor-Agnostic 1Gynecologic 1

Conditions

Desmoid Tumors 5

Interventions

Cyclophosphamide 54Specimen Handling 50Magnetic Resonance Spectroscopy 49pembrolizumab 43Doxorubicin 43Radiotherapy 42Temozolomide 37Biopsy 34Radiation 29Nivolumab 28fludarabine 23Vincristine 22Irinotecan 21Gemcitabine 21X-Rays 20Surgical Procedures, Operative 19Ifosfamide 19atezolizumab 17cabozantinib 15Ipilimumab 15olaparib 13Sunitinib 13Paclitaxel 13regorafenib 12fludarabine phosphate 12Phantoms, Imaging 12Imatinib Mesylate 12Etoposide 12Blood Specimen Collection 12Carboplatin 11

Date Range

30 days90 days1 yearAll

Options

Has results Has announcements

Clinical Trials

5 trials
RecentStart dateEnrollment
nirogacestat × Sarcoma × 1 year × Clear all
NCT05041036 2026-05-08

Individual Patient Compassionate Use of Nirogacestat

Merck Healthcare KGaA, Darmstadt, Germany, an affiliate of Merck KGaA, Darmstadt, Germany

Available
Sarcoma

Desmoid Tumors

NCT07170644 2026-05-08

A Study of Nirogacestat in Japanese Adults With Desmoid Tumors/Aggressive Fibromatosis (DT/AF)

Merck Healthcare KGaA, Darmstadt, Germany, an affiliate of Merck KGaA, Darmstadt, Germany

Phase 2 Active not recruiting
20 enrolled
Sarcoma

Desmoid Tumors

NCT07176689 2026-05-08

Nirogacestat in Premenopausal Females With Desmoid Tumor/Aggressive Fibromatosis (DT/AF)

Merck Healthcare KGaA, Darmstadt, Germany, an affiliate of Merck KGaA, Darmstadt, Germany

Phase 4 Recruiting
50 enrolled
Sarcoma

Desmoid Tumors

NCT04195399 2026-04-15

A Study of a New Drug, Nirogacestat, for Treating Desmoid Tumors That Cannot be Removed by Surgery

Children's Oncology Group

Phase 2 Active not recruiting
31 enrolled
Sarcoma

Desmoid Tumors

NCT05949099 2025-09-08

Study of Cryoablation and Nirogacestat for Desmoid Tumor

Stanford University

Phase 2 Recruiting
28 enrolled
Sarcoma

Desmoid Tumors

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